Pleomorphic adenoma is a benign lesion of the salivary glands. The most common intraoral site is the palate, with tendency to affect females between the fourth and seventh decades of life. The most reported treatment for this lesion is the surgical removal. Therefore, the aim of this report was to present the case of a 31-year-old female patient who presented a recurrence of pleomorphic adenoma and facial deformity. Recurrence was observed 22 year after first surgical treatment. Tumor involved the palatal area, nasal floor and maxillary sinus; the patient showed an augmented vertical growth of the maxilla and mandibular retrognathia with a previous compensatory orthodontic treatment. The treatment included Le Fort I osteotomy for enucleation of the tumor, upper reposition of the maxilla and a chin osteotomy for advancement. 5 year follow-up show a stable result with no recurrence. Diagnosis and treatment strategies are discussed. We concluded that this treatment is stable; Le Fort I osteotomy can help to treat the tumor and facial deformity at the same time.