The eagle syndrome (ES) is a commonly misdiagnosed condition caused primarily by it has a variety of signs and symptoms. Recent studies relate (ES) to some types of craniofacial pain that can be confused with other diseases and cause cerebrovascular accidents due to carotid artery dissection if this condition is considered a dynamic/positional pathology. It ́s important to have a multidisciplinary approach to the (ES) that allow us to understand it ́s pathophysiology, main clinical patterns, diagnostic methods, and treatments. The aim of this manuscript is to carry out an exhaustive review of the pathophysiology, clinical patterns, available diagnostic tools, treatments, and the presentation of a clinical case to guide clinicians through this underestimated condition.